Undifferentiated and aggressive tumours derived from follicular epithelium
Aetiology
- Can arise de novo or be due to dedifferentiation of another carcinoma
- Similar genetic features to papillary carcinomas and follicular carcinomas as well as p53 and β-catenin mutations
Pathophysiology
- May occur in people with a history of differentiated thyroid cancer
- Rapid growth and involvement of neck structures and death
Clinical presentation
- Features of local infiltration/compression
- Signs of distant metastases
Investigations
- Confirmation: US-FNA or biopsy
Management
- Total thyroidectomy if resectable +/- adjuvant radiochemotherapy as needed