Secondary: lack of production of ACTH by the pituitary gland
Tertiary: lack of CRH secretion by the hypothalamus
Aetiology
- Iatrogenic (excess exogenous steroid) - inhibit CRH production and ACTH production, adrenal gland becomes atrophied and is unable to produce cortisol even acutely when ACTH is given endogenously
- Pituitary/hypothalamic disorders - tumours, surgery and radiotherapy
Clinical presentation
Similar to Addison's except:
- Skin pale (no ↑ ACTH)
- Aldosterone production intact (regulated by RAAS)
- No hypertension
Investigations
- Insulin tolerance test
- CRH stimulation test
- MRI
Management
- Treat with hydrocortisone replacement (fludrocortisone unnecessary)