Idiopathic inflammatory myopathy usually occurring in men over 50 years
Aetiology
- Idiopathic
Clinical presentation
- Slowly progressive weakness of mainly distal muscles
- Characteristic thumb sparing
- Weakness of the pharyngeal muscles causes difficulty in swallowing in over 50%
Investigations
- CK - only slightly elevated
- EMG - myopathic and neuropathic changes
- MRI - changes often more distal but similar to polymyositis
- Muscle biopsy
Management
- Prednisolone
Made with Bullet