An immune-mediated glomerular disease that occurs 1–3 weeks after infection with nephritogenic strains of group A β-hemolytic Streptococcus
Aetiology
- Causative Organism
- Group A β-hemolytic Streptococcus (Streptococcus pyogenes)
- Nephritogenic Strains
- M protein types:
- Pharyngitis: M types 12, 4, 1
- Impetigo: M types 49, 55, 57
Pathophysiology
- Streptococcal infection triggers immune response
- Formation of circulating immune complexes containing streptococcal antigens (e.g., nephritis-associated plasmin receptor, streptococcal pyrogenic exotoxin B)
- Deposition of immune complexes in the glomeruli
- Activation of complement (mainly alternative pathway)
- Glomerular inflammation → ↓ GFR → hematuria, hypertension, edema
Key feature: Low serum C3 levels, which typically normalize within 6–8 weeks
Clinical presentation
Latent Period
- 1–2 weeks after streptococcal pharyngitis
- 3–6 weeks after streptococcal skin infection
Renal Manifestations (Nephritic Syndrome)
- Cola-colored or smoky urine
- Oliguria
- Mild to moderate proteinuria
- Periorbital and dependent edema
- Hypertension
Systemic Features
- Malaise
- Headache
- Nausea and vomiting
- Features of fluid overload (pulmonary edema in severe cases)
Investigations
A. Urinalysis
- Hematuria with dysmorphic RBCs
- Red blood cell casts
- Mild to moderate proteinuria
Blood Tests
- Elevated serum creatinine and urea
- Low C3 complement levels (hallmark)
- Elevated antistreptococcal antibodies:
- ASO titer (post-pharyngitis)
- Anti-DNase B (post-impetigo)
- Mild normocytic normochromic anemia
Imaging
- Renal ultrasound: normal or mildly enlarged kidneys
Renal Biopsy (Rarely Required)
Indicated if:
- Atypical presentation
- Persistent hypocomplementemia (>8 weeks)
- Rapidly progressive renal failure
Histology:
- Light microscopy: diffuse endocapillary proliferative GN
- Immunofluorescence: granular (“starry sky”) IgG and C3 deposits
- Electron microscopy: subepithelial humps (pathognomonic)
Management
Supportive Treatment (Mainstay)
- Salt and fluid restriction
- Loop diuretics for edema
- Antihypertensive therapy (e.g., calcium channel blockers)
- Careful monitoring of renal function and urine output
Antibiotic Therapy
- Amoxicillin 50mg/kg/day divided in 3 doses for 7-10 days
- Erythromycin 30mg/kg/day divided in 3 doses for 7-10 days
- Does not alter renal course, but prevents transmission and rheumatic fever
Renal Replacement Therapy
- Indicated in severe cases with:
- Refractory hyperkalemia
- Severe acidosis
- Fluid overload
- Uremic complications